Second case of postpartum acquired hemophilia A in a Korean female
نویسندگان
چکیده
Currently, there is no standard treatment for patients with T-LGL. For asymptomatic T-LGL patients with an indolent course, a wait-and-see approach can be considered [11]. In our series, all 4 patients are alive and stable, with a slowly declining trend of platelets during the more than 3-year follow-up. T-LGL clonality could not be confirmed by a T-cell receptor gene rearrangement in our cases because our facility lacks this capacity. The clinical features and laboratory findings of the T-LGL patients in our study were similar to that reported in the literature. It remains unclear if the incidence is truly low or the disease has been underdiagnosed because most cases are asymptomatic on presentation. This raises the importance of reviewing the peripheral smears in asymptomatic patients who have persistent lymphocytosis or neutropenia. Systematic long-term follow-up studies need to be performed.
منابع مشابه
The First Case of Postpartum Acquired Hemophilia A in Korea
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عنوان ژورنال:
دوره 49 شماره
صفحات -
تاریخ انتشار 2014